ｒｈＧ‐ＣＳＦとｏｘｙｍｅｔｈｏｌｏｎｅによる治療を行ったＳｈｗａｃｈｍａｎ症候群の１例

• 佐藤 雄也

  獨協医科大学第二小児科

• 斉藤 えみ

  獨協医科大学第二小児科

• 黒崎 元之

  獨協医科大学第二小児科

• 黒澤 秀光

  獨協医科大学第二小児科

• 杉田 憲一

  獨協医科大学第二小児科

• 江口 光興

  獨協医科大学第二小児科

• 古川 利温

  獨協医科大学第二小児科

書誌事項

タイトル別名

• A Case of Shwachman Syndrome Treated with rhG-CSF and Oxymetholone.

抄録

A 2-month-old boy was hospitalized with severe cough, anemia, liver dysfunction and neutropenia. He was diagnosed as having Shwachman syndrome based on the laboratory findings of anemia, neutropenia, mild thrombocytopenia, and pancreatic insufficiency. Bone marrow examination showed a decrease in the counts of nuclear cells. During the clinical course, he developed sepsis, and was treated with antibiotics and recombinant human granulocyte colony-stimulating factor (rhG-CSF). As soon as the number of neutrophils improved, he became well. To maintain the number of neutrophils and to treat anemia, rhG-CSF (50μg/m², 3 times/week) and oxymetholone (2 mg/kg/day) were administered. Severe bacterial infection was prevented and anemia gradually improved without any other treatment.

収録刊行物

• 日本小児血液学会雑誌

  日本小児血液学会雑誌 9 (6), 432-435, 1995

  特定非営利活動法人　日本小児血液・がん学会

キーワード

• Shwachman syndrome
• recombinant human granulocyte colony-stimulating factor (rhG-CSF)
• oxymetholon

詳細情報

• CRID: 1390282679318897920
• NII論文ID: 130004346343
• NII論文ID: 10012261688
• NII書誌ID: AN10080852
• DOI: 10.11412/jjph1987.9.432
• ISSN: 18844723
• ISSN: 09138706
• Web Site: https://search.jamas.or.jp/link/ui/1996208857
• 本文言語コード: ja
• データソース種別:
  • JaLC
  • CiNii Articles
• 抄録ライセンスフラグ: 使用不可