３度の後腹膜出血をきたしたＥｈｌｅｒｓ‐Ｄａｎｌｏｓ症候群ＩＶ型の１例

• 齋藤 心

  宇都宮社会保険病院外科

• 小林 伸久

  宇都宮社会保険病院外科

• 仁平 芳人

  宇都宮社会保険病院外科

• 横山 卓

  宇都宮社会保険病院外科

• 昌子 正實

  宇都宮社会保険病院外科

• 安田 是和

  自治医科大学消化器・一般外科

書誌事項

タイトル別名

• A CASE OF RETROPERITONEAL HEMORRHAGE ASSOCIATED WITH EHLERS-DANLOS SYNDROME TYPE IV

抄録

A 22-year-old man operated on twice for abdominal bleeding of unknown origin in February and August 1999 and pneumothorax in June 2002, and seen in September 2002 for severe abdominal pain was found in enhanced CT to have massive bleeding in the abdomen. Superior mesenteric arteriography showed extravasation in the perfusion area of the middle colic artery, necessitating emergency surgery. Massive peritoneal bleeding and a large mesenteric hematoma were found at the medial side of the descending colon. Bleeding was apparently due to the rupture of marginal arteries of the middle colic artery. A portion of the descending colon was necrotic, requiring resection. During surgery, because intestinal walls were too friable for anastomosis, both a transverse colostomy and a sigmoid colostomy were made in different places. The postoperative course was uneventful, witiout bleeding. The patient's elder sister underwent coronary artery bypass grafting for a coronary aneurysm when she was 24 year old. Both his clinical course and family history suggest that he had Ehlers-Danlos syndrome type IV, which may have induced repeated retroperitoneal hemorrhage.

収録刊行物

• 日本臨床外科学会雑誌

  日本臨床外科学会雑誌 65 (9), 2482-2487, 2004

  日本臨床外科学会

キーワード

• Ehlers-Danlos症候群IV型
• 後腹膜出血

詳細情報

• CRID: 1390001204845046656
• NII論文ID: 130003604217
• NII論文ID: 10013671920
• NII書誌ID: AA11189709
• DOI: 10.3919/jjsa.65.2482
• ISSN: 18825133
• ISSN: 13452843
• Web Site: http://www.jstage.jst.go.jp/article/ringe1998/65/9/65_9_2482/_pdf
• Web Site: https://search.jamas.or.jp/link/ui/2004295552
• 本文言語コード: ja
• データソース種別:
  • JaLC
  • Crossref
  • CiNii Articles
• 抄録ライセンスフラグ: 使用不可