再発を来した多発性肺軟骨性過誤腫の１例

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タイトル別名
  • A Recurrent Case of Multiple Chondromatous Hamartoma of the Lung.

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A 47-years-old man had undergone resection for multiple chondromatous hamartoma of the lung 18 years previously. After the first operation he had an asymptomatic course. An abnormal chest shadow was pointed out in July, 1994, when he was examined by his family doctor for an upper respiratory irifection and he was referred to our department. The chest CT showed a large mass with an irregular surface based on the right chest wall and a nodule in the middle lobe, and the transcutaneous biopsy from the mass revealed hyperplasia of cartilage, identical to the findings of the previously resected chondromatous hamartoma. Multiple chondromatous hamartoma of the lung is a rare disease, and only 15 cases have been reported in the world. Three main characteristics of this disease are as follows: the age of onset is relatively young (mean age of onset is 34.3 years old); the recurrence rate is very high (6 of 15 cases, 40%) and the period between first onset and recurrence is very long (the mean period of all recurrence cases is 12.7 years); young females are often complicated by gastric leiomyogenic neoplasms, especially gastric leiomyoblastoma, and extraadrenal paragangliomas. These three diseases, including chondromatous hamartoma of the lung, are described as “Carney syndrome”.

収録刊行物

  • 肺癌

    肺癌 36 (1), 49-53, 1996

    特定非営利活動法人 日本肺癌学会

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