完全内臓逆位を併存し腸間膜線維腫症を伴った不完全型Ｇａｒｄｎｅｒ症候群の１例

• 木下 敬史

  小牧市民病院外科

• 藤井 努

  名古屋大学大学院消化器外科学

• 末永 裕之

  小牧市民病院外科

• 丸山 浩高

  総合病院中津川市民病院外科

• 桐山 幸三

  小牧市民病院外科

• 中尾 昭公

  名古屋大学大学院消化器外科学

書誌事項

タイトル別名

• A CASE OF MESENTERIC FIBROMATOSIS IN INCOMPLETE GARDNER'S SYNDROME WITH TOTAL SITUS INVERSUS

抄録

We report a case of mesenteric fibromatosis with incomplete Gardner's syndrome and total situs inversus. A 34-year-old female was found to have a history of polyposis coli and dextrocardia in childhood. Intraabdominal tumor was detected at the time of left oophorectomy in July 2002, and she was referred to our hospital. Abdominal CT and MRI showed total situs inversus and a 10×5×4cm tumor in the abdomen. Barium enema roentgenogram showed numerous small polyps. Laparotomy was performed in August 2002. In the operation we paid close attention to the mirror image. The tumor was located in the mesostenium and had invaded the small intestine and duodenum. The entire tumor and segment of the small intestine and duodenum were resected. This case had polyposis coli but no osteoma, and the histological findings of the tumor revealed a mesenteric fibromatosis. Thus, we made a diagnosis of incomplete Gardner's syndrome. The tumor recurred one year after the operation. Laparotomy revealed unresectable recurrent mesenteric fibromatosis.

収録刊行物

• 日本臨床外科学会雑誌

  日本臨床外科学会雑誌 67 (7), 1689-1694, 2006

  日本臨床外科学会

キーワード

• 腸間膜線維腫症
• Gardner症候群
• 内臓逆位症

詳細情報

• CRID: 1390282679826016384
• NII論文ID: 130003605134
• NII論文ID: 10017656697
• NII書誌ID: AA11189709
• DOI: 10.3919/jjsa.67.1689
• ISSN: 18825133
• ISSN: 13452843
• ISSN: http://id.crossref.org/issn/13452843
• Web Site: http://www.jstage.jst.go.jp/article/ringe1998/67/7/67_7_1689/_pdf
• Web Site: https://search.jamas.or.jp/link/ui/2006260293
• 本文言語コード: ja
• データソース種別:
  • JaLC
  • Crossref
  • CiNii Articles
• 抄録ライセンスフラグ: 使用不可