膵後面後腹膜リンパ管筋腫の1例 [in Japanese] A CASE OF LYMPHANGIOMYOMA OF THE RETROPERITONEUM LOCATED ON THE POSTERIOR SURFACE OF THE PANCREAS [in Japanese]
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リンパ管筋腫(Lymphangiomyoma: LAM)はリンパ管周囲の平滑筋が増殖する良性腫瘍で女性骨盤内後腹膜のリンパ節が好発部位とされ,時として肺,縦隔内に広範に進展し,致死的な経過をとる極めて稀な疾患である.<br> われわれは膵後面の後腹膜に限局したLAMを経験したので報告する.症例は40歳,女性.平成13年12月人間ドックで腹部USにて膵後面に占拠性病変を指摘され,当科紹介受診となった.手術所見では,腫瘤は下行大動脈と下大静脈の間を占拠し,被膜をもち境界明瞭で浸潤を認めず,一塊に摘出しえた.術後病理所見よりLAMと診断した.術後48カ月目の現在再発徴候なく生存中である.後腹膜病変のみのLAMは本邦では9例目と極めて稀であり,文献的考察を加えて報告する.
Lymphangiomyoma (LAM) is a rare entity occurring mainly in women in the reproductive generations, and is often accompanied with multiple lesions in the lower retroperitoneum and/or lethal spread to the lung and mediastinum. On the other hand, there have been only few reports of LAM confined within the retroperitoneum. We present a case of LAM of the retroperitoneum located on the posterior surface of the pancreas which is the ninth case, together with a review of the reported cases in Japan.<br> A 40-year-old woman was admitted to the hospital because of a retroperitoneal tumor on the posterior surface of the pancreas. Examinations revealed a polycystic mass located between the descending aorta and the inferior vena cava, with clear borders from adjacent organs. A diagnosis of retroperitoneal tumor was made and laparotomy was performed. The cystic tumor, filled with lymphatic fluid, did not invaded the surrounding tissues and was dissected enbloc easily. LAM was diagnosed with histological examinations postoperatively. The patient has been well without recurrence for 48 months after the operation.
- The journal of the Japanese Practical Surgeon Society
The journal of the Japanese Practical Surgeon Society 67(10), 2453-2456, 2006-10-25
Japan Surgical Association