顎形態異常を骨延長法により治療した基底細胞母斑症候群の1例 A case of basal cell nevus syndrome with jaw deformity treated by maxillary distraction osteogenesis
Basal cell nevus syndrome (BCNS) is frequently accompanied by multiple maxillomandibular cysts. This disease is known to cause several types of maxillofacial deformity, but there are few reports of orthognathic surgery in patients with BCNS. A patient with BCNS who underwent maxillary distraction osteogenesis is described. The patient was a 19-year-old man. He underwent palatoplasty for cleft palate while he was an infant. Maxillary hypoplasia subsequently developed. Le Fort I osteotomy and anterior alveolar osteotomy of the mandible were performed. A RED system and lateral expansion device were used for maxillary advancement and palatal widening. The total advancement was 15mm, and the total lateral expansion was 6 mm. After distraction, orthodontic treatment was continued. At present, 3 years after distraction, an excellent facial outline and occlusal condition have been obtained. After the operation, we have kept the patient under close observation.
日本口腔外科学会雑誌 53(3), 192-196, 2007-03-20
Japanese Society of Oral and Maxillofacial Surgeons