A case of basal cell nevus syndrome with jaw deformity treated by maxillary distraction osteogenesis

• MARUKAWA Kohei

  Oral and Maxlllofacial Surgery, Department of Cell and Tissue Biology, Dividion of Cancer Science, Kanazawa University Graduate School of Medical Science

• UEKI Koichiro

  Oral and Maxlllofacial Surgery, Department of Cell and Tissue Biology, Dividion of Cancer Science, Kanazawa University Graduate School of Medical Science

• OHARA Teruhisa

  Oral and Maxlllofacial Surgery, Department of Cell and Tissue Biology, Dividion of Cancer Science, Kanazawa University Graduate School of Medical Science

• TAKATSUKA Shigeyuki

  Oral and Maxlllofacial Surgery, Department of Cell and Tissue Biology, Dividion of Cancer Science, Kanazawa University Graduate School of Medical Science

• NAKAGAWA Kiyomasa

  Oral and Maxlllofacial Surgery, Department of Cell and Tissue Biology, Dividion of Cancer Science, Kanazawa University Graduate School of Medical Science

• YAMAMOTO Etsuhide

  Oral and Maxlllofacial Surgery, Department of Cell and Tissue Biology, Dividion of Cancer Science, Kanazawa University Graduate School of Medical Science

Bibliographic Information

Other Title

• 顎形態異常を骨延長法により治療した基底細胞母斑症候群の１例
• ガク ケイタイ イジョウ オ コツ エンチョウホウ ニ ヨリ チリョウシタ キテイ サイボウ ボハン ショウコウグン ノ 1レイ

Abstract

Basal cell nevus syndrome (BCNS) is frequently accompanied by multiple maxillomandibular cysts. This disease is known to cause several types of maxillofacial deformity, but there are few reports of orthognathic surgery in patients with BCNS. A patient with BCNS who underwent maxillary distraction osteogenesis is described. The patient was a 19-year-old man. He underwent palatoplasty for cleft palate while he was an infant. Maxillary hypoplasia subsequently developed. Le Fort I osteotomy and anterior alveolar osteotomy of the mandible were performed. A RED system and lateral expansion device were used for maxillary advancement and palatal widening. The total advancement was 15mm, and the total lateral expansion was 6 mm. After distraction, orthodontic treatment was continued. At present, 3 years after distraction, an excellent facial outline and occlusal condition have been obtained. After the operation, we have kept the patient under close observation.

Journal

• Japanese Journal of Oral and Maxillofacial Surgery

  Japanese Journal of Oral and Maxillofacial Surgery 53 (3), 192-196, 2007

  Japanese Society of Oral and Maxillofacial Surgeons

Keywords

• basal cell nevus syndrome
• cleft lip and palate
• jaw deformity
• maxillary distraction osteogenesis

Details

• CRID: 1390001206533782528
• NII Article ID: 10018858317
• NII Book ID: AN00189163
• DOI: 10.5794/jjoms.53.192
• ISSN: 21861579
• ISSN: 00215163
• NDL BIB ID: 8755120
• Web Site: https://ndlsearch.ndl.go.jp/books/R000000004-I8755120
• Web Site: https://search.jamas.or.jp/link/ui/2007153855
• Text Lang: ja
• Data Source:
  • JaLC
  • NDL
  • Crossref
  • CiNii Articles
  • KAKEN
• Abstract License Flag: Disallowed