A Case of Lipofibromatous Hamartoma of the Median Nerve.

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  • TERAUCHI Masami
    Division of Plastic and Reconstructive Surgery, Numazu Municipal Hospital

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  • Ｌｉｐｏｆｉｂｒｏｍａｔｏｕｓ　Ｈａｍａｒｔｏｍａ　ｏｆ　ｔｈｅ　Ｍｅｄｉａｎ　Ｎｅｒｖｅの１例

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Abstract

Lipofibromatous hamartoma of the nerve (LFH) is a rare benign tumor-like nodule characterized by an overgrowth of fibrous and adipose tissue of the peripheral nerve. It frequently affects the median nerve, and is clinically characterized by peripheral subcutaneous diffuse swelling of the extremities. I describe a 16-year-old male adolescent who presented with the main complaint of swelling from the palm to the index finger and was diagnosed to have LFH which affected the median and index digital nerve. LFH is considered to be due to a non-neoplastic proliferation of fibrous and adipose tissues, which is also composed of the peripheral nerves in the extremities. Since Mason reported the first case in 1953, about 100 cases have been reported in various countries, including Japan. Diagnostic imaging methods, such as CT or MRI, have been suggested to be useful for the diagnosis of LFH, although its actual diagnosis is often made based on the intra-operative and histopathological findings. Various therapies have been proposed, as follows: a microscopic resection of the nodule; a resection of the nerve and nodule followed by neuroanastomosis or nerve grafting; a resection of the nerve and nodule; and in the case of carpal tunnel syndrome, decompression by releasing the carpal tunnel. A partial excision of the nerve and nodule was performed in this case, and no serious neurological deficiency symptom was observed after surgery.

Journal

  • Nishi Nihon Hifuka

    Nishi Nihon Hifuka 64 (2), 187-189, 2002

    Western Division of Japanese Dermatological Association

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