Hypersomnia as a Presentation of Paraneoplastic Limbic Encephalitis in a Patient with Adult T Cell Leukemia/lymphoma

  • Katsuya Hiroo
    Departments of Oncology, Infectious Disease and Endocrinology, Fukuoka University School of Medicine
  • Ishitsuka Kenji
    Departments of Oncology, Infectious Disease and Endocrinology, Fukuoka University School of Medicine
  • Sasaki Hidenori
    Departments of Oncology, Infectious Disease and Endocrinology, Fukuoka University School of Medicine
  • Wakamatsu Shinichi
    Departments of Oncology, Infectious Disease and Endocrinology, Fukuoka University School of Medicine
  • Inoue Hirosato
    Neurology, Fukuoka University School of Medicine
  • Takamatsu Yasushi
    Departments of Oncology, Infectious Disease and Endocrinology, Fukuoka University School of Medicine
  • Suzumiya Junji
    Departments of Oncology, Infectious Disease and Endocrinology, Fukuoka University School of Medicine
  • Tsuboi Yoshio
    Neurology, Fukuoka University School of Medicine
  • Tamura Kazuo
    Departments of Oncology, Infectious Disease and Endocrinology, Fukuoka University School of Medicine

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Other Title
  • 傍腫瘍性辺縁系脳炎による突発性睡眠を発症した急性型成人T細胞白血病の1例
  • ボウシュヨウセイ ヘンエンケイ ノウエン ニ ヨル トッパツセイ スイミン オ ハッショウシタ キュウセイガタ セイジン Tサイボウ ハッケツビョウ ノ 1レイ

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Abstract

傍腫瘍性辺縁系脳炎(paraneoplastic limbic encephalitis,PLE)は,悪性腫瘍に伴う自己免疫機序を介して生じる傍腫瘍性神経症候群の1つで,記憶障害や情動変化,痙攣など多彩な症状を呈する.原疾患としては肺小細胞癌や精巣腫瘍,乳癌などが多く1),成人T細胞白血病(adult T cell leukemia/lymphoma,ATLL)での合併は報告されていない.我々はPLEを合併したATLLの症例を経験したので報告する.<br>

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