偽性低アルドステロン症Ⅰ型を呈した両側原発性閉塞性巨大尿管症の1例

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タイトル別名
  • Pseudohypoaldosteronism Type 1 in an Infant with Bilateral Primary Obstructive Megaureter : A Case Report
  • 偽性低アルドステロン症1型を呈した両側原発性閉塞性巨大尿管症の1例
  • ギセイ テイアルドステロンショウ 1ガタ オ テイシタ リョウソク ゲンパツセイ ヘイソクセイ キョダイ ニョウカンショウ ノ 1レイ

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A 35-day-old male infant was referred to our hospital for bilateral hydroureteronephrosis on postnatal ultrasonography. He was born at 37 weeks and 2 days of gestation, weighing 2, 765 g. He was diagnosed with bilateral primary obstructive megaureter. During observation, at 3 months and 2 weeks of age, he presented with dehydration and showed hyponatremia and hyperkalemia. An endocrinological examination led to a diagnosis of pseudohypoaldosteronism type 1 (PHA1). After bilateral percutaneous nephrostomy, PHA1 resolved. He underwent bilateral ureteral tapering and ureteroneocystostomy at 5 months and 3 weeks of age. Since PHA1 recurred after removal of urethral catheter, urethral catheter and bilateral double-J-stent was kept until 8 months old. He was followed-up until 3 years old with no signs of PHA1 recurrence. For an infant with obstructive uropathy or vesicoureteral reflux showing hyponatremia and hyperkalemia, PHA1 should be considered.

収録刊行物

  • 泌尿器科紀要

    泌尿器科紀要 57 (4), 193-197, 2011-04

    泌尿器科紀要刊行会

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