Atrial Right-to-left Shunt without Pulmonary Hypertension in a Patient with Biventricular Non-compaction Cardiomyopathy Accompanied by Ventricular and Atrial Septal Defects

  • Sakan Hirokazu
    The First Department of Internal Medicine, Nara Medical University, Japan
  • Okayama Satoshi
    The First Department of Internal Medicine, Nara Medical University, Japan
  • Uemura Shiro
    The First Department of Internal Medicine, Nara Medical University, Japan
  • Somekawa Satoshi
    The First Department of Internal Medicine, Nara Medical University, Japan
  • Ishigami Ken-ichi
    The First Department of Internal Medicine, Nara Medical University, Japan
  • Takeda Yukiji
    The First Department of Internal Medicine, Nara Medical University, Japan
  • Kawata Hiroyuki
    The First Department of Internal Medicine, Nara Medical University, Japan
  • Horii Manabu
    The First Department of Internal Medicine, Nara Medical University, Japan
  • Fujimoto Shinichi
    Education Development Center, Nara Medical University, Japan
  • Saito Yoshihiko
    The First Department of Internal Medicine, Nara Medical University, Japan

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抄録

Echocardiography and magnetic resonance imaging revealed biventricular non-compaction cardiomyopathy with ventricular (VSD) and atrial (ASD) septal defects in an unconscious, 23-year-old hypoxemic man. Doppler echocardiography showed a left-to-right shunt across the VSD and a right-to-left shunt across the ASD. Cardiac catheterization revealed elevated right atrial pressure, although pulmonary pressure was normal. We considered that the atrial right-to-left shunt had induced the hypoxemia, which was related mainly to right ventricular dysfunction in this biventricular non-compaction cardiomyopathy, but it was not related to pulmonary hypertension.<br>

収録刊行物

  • Internal Medicine

    Internal Medicine 50 (16), 1747-1751, 2011

    一般社団法人 日本内科学会

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