Periodic spasmsを呈する食事誘発性発作が認められた5 p-症候群の1例

• 澤井 康子

  国立病院機構奈良医療センターてんかんセンター

• 丸山 信之

  国立病院機構奈良医療センターてんかんセンター

• 星田 徹

  国立病院機構奈良医療センターてんかんセンター

書誌事項

タイトル別名

• Eating-induced Epilepsy with Periodic Spasms in a Patient with 5 p- syndrome

抄録

Various cases of eating-induced epilepsy have been reported. A 7-year-old male 5 p-syndrome patient with symptomatic generalized epilepsy was admitted and long-term video electroencephalography monitoring was performed. He showed atypical absence, myoclonus, non-periodic and periodic spasms. His periodic spasms were characteristic because they were induced by eating. MRI showed slight hypoplasty of the left frontal operculum. The abnormal opercular formation observed in this case is consistent with the findings observed in previously reported cases of eating epilepsy. Furthermore, white matter degeneration in the pons and midbrain were suspected on the basis of the MRI findings. The brain stem degeneration observed in this case may be associated with the development of spasms.<br>

収録刊行物

• てんかん研究

  てんかん研究 30 (3), 511-516, 2013

  一般社団法人 日本てんかん学会

キーワード

• periodic spasms
• eating epilepsy
• 5 p-
• long-term video EEG monitoring

詳細情報

• CRID: 1390001204517606784
• NII論文ID: 10031138432
• NII書誌ID: AN10043823
• DOI: 10.3805/jjes.30.511
• ISSN: 13475509
• ISSN: 09120890
• Web Site: https://search.jamas.or.jp/link/ui/2013165734
• 本文言語コード: ja
• データソース種別:
  • JaLC
  • Crossref
  • CiNii Articles
• 抄録ライセンスフラグ: 使用不可