中大脳動脈閉塞症をきたした弾力線維性仮性黄色腫の１例

• 山中 龍也

  富山県立中央病院脳神経外科 新潟大学脳研究所脳神経外科

• 寺林 征

  富山県立中央病院脳神経外科

• 新井田 広仁

  富山県立中央病院脳神経外科 新潟大学脳研究所脳神経外科

• 三輪 淳夫

  同 臨床病理科

• 杉山 義昭

  富山県立中央病院脳神経外科

書誌事項

タイトル別名

• A case of pseudoxanthoma elasticum associated with middle cerebral artery occlusion.

抄録

Pseudoxanthoma elasticum (PXE) is a hereditary disorder with an autosomal dominant or recessive mode of transmission. PXE is now generally believed to be a disease which is mainly characterized with a genetically determined degeneration of the elastic tissue throughout the body, with secondary calcium deposition. The disease presents clinically three major manifestations : (1) skin lesion, characterized by yellowish papules, (2) angioid streakes of the retina, (3) cardiovascular changes which include symptoms of vascular insufficiency and hemorrhage involving different organs.<BR>In this report, a case of PXE associated with middle cerebral artery occlusion is described. A 52-year-old woman was complicated by dysarthria and left hemiparesis. Angiography showed right middle cerebral artery occlusion. The ischemic attack was presumably due to cerebrovascular involvement of PXE which was confirmed by skin biopsy. Thirty-three cases of PXE with the involvement of the central nervous system reported in the literature were analyzed for characteristics of this disease.

収録刊行物

• 脳卒中

  脳卒中 13 (3), 175-179, 1991

  一般社団法人 日本脳卒中学会

キーワード

• pseudoxanthoma elasticum
• middle cerebral artery
• angioid streaks

詳細情報

• CRID: 1390001204640153216
• NII論文ID: 130003630927
• DOI: 10.3995/jstroke.13.175
• ISSN: 18831923
• ISSN: 09120726
• 本文言語コード: ja
• データソース種別:
  • JaLC
  • Crossref
  • CiNii Articles
• 抄録ライセンスフラグ: 使用不可