前庭機能検査を施行した小児の前庭水管拡大症の 2 例

• 菅谷 明子

  岡山大学大学院医歯薬学総合研究科　耳鼻咽喉・頭頸部外科学

• 前田 幸英

  岡山大学大学院医歯薬学総合研究科　耳鼻咽喉・頭頸部外科学

• 片岡 祐子

  岡山大学大学院医歯薬学総合研究科　耳鼻咽喉・頭頸部外科学

• 平井 美紗都

  岡山済生会総合病院　耳鼻咽喉科

• 福島 邦博

  岡山大学大学院医歯薬学総合研究科　耳鼻咽喉・頭頸部外科学

• 西﨑 和則

  岡山大学大学院医歯薬学総合研究科　耳鼻咽喉・頭頸部外科学

書誌事項

タイトル別名

• Vertigo and vestibular functions of two patients with EVA

抄録

  Enlarged vestibular aqueduct (EVA) is one of the most common congenital inner ear malformations. Vertigo may accompany fluctuating hearing loss, but its evaluation is usually difficult because many of the patients are very young. We report the results of vestibular function of two cases of bilateral EVA with vertigo in children.<br/>  Case 1: A 7-year-old boy with a bilateral congenital hearing loss was referred to our hospital because of repeated episodes of vertigo. He had worn hearing aids bilaterally since he was 3 months old. At the age of four, he first complained of vertigo suddenly. Pure tone audiometry revealed hearing deterioration in the right ear, and intravenous administration of corticosteroid was commenced immediately. Similar attacks were repeated twice after this first episode. Temporal bone computed tomography (CT) imaging detected bilateral EVA. Compound heterozygous mutations in SLC26A4, H723R, IVS7–2G>A, were later identified. Electronystagmography (ENG), which was taken after he recovered from vertigo, showed elimination of bilateral caloric responses.<br/>  Case 2: An 8-year-old boy with a progressive hearing loss was referred to our hospital for episodic vertigo. He suddenly had difficulty in conversation at the age of four and had received corticosteroid therapy. Brain magnetic resonance imaging (MRI) did not demonstrate any abnormalities in the brain parenchyma. Auditory brainstem response (ABR) revealed bilateral hearing loss, and he began to wear a hearing aid in his right ear. He had another attack with deterioration of hearing in his left ear, and intervenous corticosteroid therapy was administrated. The temporal bone CT imaging revealed bilateral EVA. ENG with no vertigo showed decreased right caloric response.

収録刊行物

• Pediatric Otorhinolaryngology Japan

  Pediatric Otorhinolaryngology Japan 31 (3), 299-306, 2010

  日本小児耳鼻咽喉科学会

キーワード

• 前庭水管拡大症
• 回転性めまい
• 小児

詳細情報

• CRID: 1390282680441707264
• NII論文ID: 130004672192
• NII論文ID: 10027696079
• NII書誌ID: AN10044779
• DOI: 10.11374/shonijibi.31.299
• ISSN: 21865957
• ISSN: 09195858
• Web Site: https://search.jamas.or.jp/link/ui/2011192271
• 本文言語コード: ja
• データソース種別:
  • JaLC
  • CiNii Articles
• 抄録ライセンスフラグ: 使用不可