The Change of Grip Strength in a Patient with Congenital Myotonic Dystrophy Over a 4-year Period
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- Kikuchi Shin
- Department of Anatomy 1, Sapporo Medical University School of Medicine
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- Kozuka Naoki
- School of Health Sciences, Sapporo Medical University
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- Uchida Eiji
- Department of Human Science, Faculty of Human Studies, Taisho University
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- Ninomiya Takafumi
- Department of Anatomy 1, Sapporo Medical University School of Medicine
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- Tatsumi Haruyuki
- Department of Anatomy 1, Sapporo Medical University School of Medicine
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- Takeda Hidekatsu
- School of Health Sciences, Sapporo Medical University
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- Tachi Nobutada
- School of Health Sciences, Sapporo Medical University
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抄録
Myotonic dystrophy (MyD) is a neuromuscular disease that is autosomal dominant and the most common form of muscular dystrophy affecting adults. The clinical features of MyD include a multisystemic disorder characterized by myotonia, progressive muscle weakness and wasting, cataracts, premature balding and mental retardation. The most severe type of MyD is classified as congenital MyD (CMyD). The muscle weakness in CMyD is very severe, but muscle development can be observed in the period of growth. However, no clinical case of this type has been reported yet. Therefore, we report on a girl with CMyD who had an increase in muscle strength over a four-year period. The girl with CMyD participated in this study from the age of 9 to the age of 12. The measurement of muscle strength was recorded as the maximum score of grip strength with the use of dynamometers. Grip strength was assessed once a year by the same two physical therapists. Grip strength of CMyD for each year was markedly weak when compared with the normal controls, but muscle strength changed within some specific growth areas. The muscle weakness in CMyD was remarkable, but the result showed that specific muscle strength of CMyD in childhood was actually increased.<br>
収録刊行物
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- Journal of the Japanese Physical Therapy Association
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Journal of the Japanese Physical Therapy Association 11 (1), 23-27, 2008
公益社団法人 日本理学療法士協会
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詳細情報 詳細情報について
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- CRID
- 1390282679446189952
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- NII論文ID
- 130004677670
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- ISSN
- 21888361
- 13441272
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- 本文言語コード
- en
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- データソース種別
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- JaLC
- Crossref
- CiNii Articles
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- 抄録ライセンスフラグ
- 使用不可