An Adult Case of Polysplenia Syndrome Associated with Sinus Node Dysfunction, Dextrocardia, and Systemic Venous Anomalies
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- Fukuda Kentaro
- Department of Cardiology, Juntendo University Nerima Hospital, Japan
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- Onda Toshihito
- Department of Cardiology, Juntendo University Nerima Hospital, Japan
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- Kimura Yuki
- Department of Cardiology, Juntendo University Nerima Hospital, Japan
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- Miura Seiji
- Department of Cardiology, Juntendo University Nerima Hospital, Japan
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- Matsumori Rie
- Department of Cardiology, Juntendo University Nerima Hospital, Japan
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- Masaki Yoshiyuki
- Department of Cardiology, Juntendo University Nerima Hospital, Japan
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- Nishino Akihisa
- Department of Cardiology, Juntendo University Nerima Hospital, Japan
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- Inoue Kenji
- Department of Cardiology, Juntendo University Nerima Hospital, Japan
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- Fujiwara Yasumasa
- Department of Cardiology, Juntendo University Nerima Hospital, Japan
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- Sumiyoshi Masataka
- Department of Cardiology, Juntendo University Nerima Hospital, Japan
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抄録
A 54-year-old woman was referred to our hospital for symptomatic sinus bradyarrhythmia with a sinus pause of 8 seconds. She was diagnosed with dextrocardia during childhood and discovered to have heterotaxy syndrome when she had an appendectomy during her teenager years. Chest and abdominal examinations by computed tomography showed multiple spleens located on the right side and abnormal drainages of the superior and inferior vena cava. Left isomerism was diagnosed by bilaterally bilobed lungs. Because of a patent bilateral superior vena cava, pacemaker leads were implanted using the right cephalic vein approach. Her fainting symptoms disappeared after pacemaker implantation.<br>
収録刊行物
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- Internal Medicine
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Internal Medicine 54 (9), 1071-1074, 2015
一般社団法人 日本内科学会
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詳細情報
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- CRID
- 1390282679853163136
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- NII論文ID
- 130005068302
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- ISSN
- 13497235
- 09182918
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- PubMed
- 25948350
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- 本文言語コード
- en
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- データソース種別
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- JaLC
- Crossref
- PubMed
- CiNii Articles
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- 抄録ライセンスフラグ
- 使用不可