An Adult Case of Polysplenia Syndrome Associated with Sinus Node Dysfunction, Dextrocardia, and Systemic Venous Anomalies

  • Fukuda Kentaro
    Department of Cardiology, Juntendo University Nerima Hospital, Japan
  • Onda Toshihito
    Department of Cardiology, Juntendo University Nerima Hospital, Japan
  • Kimura Yuki
    Department of Cardiology, Juntendo University Nerima Hospital, Japan
  • Miura Seiji
    Department of Cardiology, Juntendo University Nerima Hospital, Japan
  • Matsumori Rie
    Department of Cardiology, Juntendo University Nerima Hospital, Japan
  • Masaki Yoshiyuki
    Department of Cardiology, Juntendo University Nerima Hospital, Japan
  • Nishino Akihisa
    Department of Cardiology, Juntendo University Nerima Hospital, Japan
  • Inoue Kenji
    Department of Cardiology, Juntendo University Nerima Hospital, Japan
  • Fujiwara Yasumasa
    Department of Cardiology, Juntendo University Nerima Hospital, Japan
  • Sumiyoshi Masataka
    Department of Cardiology, Juntendo University Nerima Hospital, Japan

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抄録

A 54-year-old woman was referred to our hospital for symptomatic sinus bradyarrhythmia with a sinus pause of 8 seconds. She was diagnosed with dextrocardia during childhood and discovered to have heterotaxy syndrome when she had an appendectomy during her teenager years. Chest and abdominal examinations by computed tomography showed multiple spleens located on the right side and abnormal drainages of the superior and inferior vena cava. Left isomerism was diagnosed by bilaterally bilobed lungs. Because of a patent bilateral superior vena cava, pacemaker leads were implanted using the right cephalic vein approach. Her fainting symptoms disappeared after pacemaker implantation.<br>

収録刊行物

  • Internal Medicine

    Internal Medicine 54 (9), 1071-1074, 2015

    一般社団法人 日本内科学会

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