Atypical Subacute Recurrence of Catastrophic Antiphospholipid Syndrome in a Japanese Female Patient
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- Horikoshi Masanobu
- Department of Allergy and Rheumatic Diseases, Japanese Red Cross Medical Center, Japan
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- Inokuma Shigeko
- Department of Allergy and Rheumatic Diseases, Japanese Red Cross Medical Center, Japan
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- Matsubara Erika
- Department of Allergy and Rheumatic Diseases, Japanese Red Cross Medical Center, Japan
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- Honda Yasunori
- Department of Allergy and Rheumatic Diseases, Japanese Red Cross Medical Center, Japan
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- Okada Rika
- Department of Allergy and Rheumatic Diseases, Japanese Red Cross Medical Center, Japan
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- Kobuna Mika
- Department of Allergy and Rheumatic Diseases, Japanese Red Cross Medical Center, Japan
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- Miura Yoko
- Department of Allergy and Rheumatic Diseases, Japanese Red Cross Medical Center, Japan
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- Kobayashi Shoko
- Department of Allergy and Rheumatic Diseases, Japanese Red Cross Medical Center, Japan
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- Kawai Shigeo
- Department of Pathology, Japanese Red Cross Medical Center, Japan
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- Kumasaka Toshio
- Department of Pathology, Japanese Red Cross Medical Center, Japan
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抄録
Catastrophic antiphospholipid syndrome (CAPS) survivors rarely relapse. We herein report a case of a second CAPS episode with an unusual subacute course and no microangiopathic hemolytic anemia (MAHA), a common CAPS symptom. During the first episode, the 69-year-old woman responded well to high-dose glucocorticoids and plasma exchange. On relapse, these treatments plus rituximab were ineffective and she died of multi-organ failure and bacterial cholangitis. The absence of MAHA and a subacute course do not exclude a CAPS recurrence.<br>
収録刊行物
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- Internal Medicine
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Internal Medicine 54 (22), 2923-2927, 2015
一般社団法人 日本内科学会