Two Kinds of Cystic Lung Lesions with Pulmonary Lymphangioleiomyomatosis in a Male
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- Yamanaka Sumitaka
- Nissan Kohseikai Institute of Medicine, Pneumothorax Research Center, Tokyo, Japan
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- Mizobuchi Teruaki
- Nissan Kohseikai Institute of Medicine, Pneumothorax Research Center, Tokyo, Japan
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- Kurihara Masatoshi
- Nissan Kohseikai Institute of Medicine, Pneumothorax Research Center, Tokyo, Japan
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抄録
A 34-year-old male with frequent recurrence of right pneumothorax was admitted to our hospital. He was a current smoker and outwardly male without genital aplasia. He was diagnosed as tuberous sclerosis complex (TSC) at 2 year-old and underwent transcatheter arterial embolization for right renal hemorrhage due to renal tumor 2 years ago. Chest Computed Tomography showed that he had multiple tiny round cystic lesions with thin wall in both lungs. The recurrent pneumothorax was expected to be associated with TSC-Lymphangioleiomyomatosis (LAM). Video-assisted thoracic surgery was successfully performed. The operative and histological findings revealed that the bullae were classified into two groups; emphysematous bullae and bullae due to LAM. His postoperative course was uneventful. TSC-LAM is extremely rare, but in some cases the clinical recognition might be escaped due to subtle findings of bullae in early LAM, resulting in diagnosis as spontaneous pneumothorax.
収録刊行物
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- Annals of Thoracic and Cardiovascular Surgery
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Annals of Thoracic and Cardiovascular Surgery 23 (1), 36-39, 2017
Annals of Thoracic and Cardiovascular Surgery 編集委員会