AA-negative and Kappa-positive Amyloidosis in a Patient with Rheumatoid Arthritis
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- Ueno Toshiharu
- Nephrology Center, Toranomon Hospital Kajigaya, Japan
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- Sumida Keiichi
- Nephrology Center, Toranomon Hospital Kajigaya, Japan
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- Hoshino Junichi
- Nephrology Center, Toranomon Hospital Kajigaya, Japan
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- Suwabe Tatsuya
- Nephrology Center, Toranomon Hospital Kajigaya, Japan
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- Mise Koki
- Nephrology Center, Toranomon Hospital Kajigaya, Japan
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- Hazue Ryo
- Nephrology Center, Toranomon Hospital Kajigaya, Japan
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- Hayami Noriko
- Nephrology Center, Toranomon Hospital Kajigaya, Japan
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- Hiramatsu Rikako
- Nephrology Center, Toranomon Hospital Kajigaya, Japan
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- Kawada Masahiro
- Nephrology Center, Toranomon Hospital Kajigaya, Japan
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- Imafuku Aya
- Nephrology Center, Toranomon Hospital Kajigaya, Japan
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- Hasegawa Eiko
- Nephrology Center, Toranomon Hospital Kajigaya, Japan
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- Sawa Naoki
- Nephrology Center, Toranomon Hospital Kajigaya, Japan
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- Takaichi Kenmei
- Nephrology Center, Toranomon Hospital Kajigaya, Japan Okinaka Memorial Institute for Medical Research, Toranomon Hospital, Japan
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- Kinowaki Keiichi
- Department of Pathology, Toranomon Hospital, Japan
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- Ohashi Kenichi
- Department of Pathology, Toranomon Hospital, Japan
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- Fujii Takeshi
- Department of Pathology, Toranomon Hospital, Japan
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- Nishida Aya
- Department of Hematology, Toranomon Hospital Kajigaya, Japan
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- Ubara Yoshifumi
- Nephrology Center, Toranomon Hospital Kajigaya, Japan Okinaka Memorial Institute for Medical Research, Toranomon Hospital, Japan
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抄録
<p>A 57-year-old Japanese woman with a 5-year history of rheumatoid arthritis (RA) was admitted to our hospital for an evaluation of nephrotic range proteinuria (4.8 g/day). A renal biopsy led to the diagnosis of amyloidosis according to strong positivity for Congo red staining and the detection of microfibrillar structures on electron microscopy that were negative for AA and positive for kappa light chain. Combination therapy with high-dose melphalan and autologous stem cell transplantation was performed according to the regimen for AL amyloidosis. Her proteinuria and RA subsided, but relapsed after 3 years. This is the first report regarding kappa light chain amyloidosis in an RA patient. </p>
収録刊行物
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- Internal Medicine
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Internal Medicine 55 (17), 2491-2495, 2016
一般社団法人 日本内科学会