A Cryptogenic Case of Fulminant Fibrosing Organizing Pneumonia

  • Kobayashi Takehiko
    Department of Internal Medicine, National Hospital Organization Kinki-Chuo Chest Medical Center, Japan
  • Kitaichi Masanori
    Clinical Research Center, National Hospital Organization Kinki-Chuo Chest Medical Center, Japan Department of Pathology, National Hospital Organization Kinki-Chuo Chest Medical Center, Japan Department of Pathology, National Hospital Organization Minami Wakayama Medical Center, Japan
  • Tachibana Kazunobu
    Department of Internal Medicine, National Hospital Organization Kinki-Chuo Chest Medical Center, Japan Clinical Research Center, National Hospital Organization Kinki-Chuo Chest Medical Center, Japan
  • Kishimoto Yutaro
    Department of Internal Medicine, National Hospital Organization Kinki-Chuo Chest Medical Center, Japan Department of Respiratory Medicine, Iwata City Hospital, Japan
  • Inoue Yasushi
    Department of Internal Medicine, National Hospital Organization Kinki-Chuo Chest Medical Center, Japan
  • Kagawa Tomoko
    Department of Internal Medicine, National Hospital Organization Kinki-Chuo Chest Medical Center, Japan Clinical Research Center, National Hospital Organization Kinki-Chuo Chest Medical Center, Japan
  • Maekura Toshiya
    Department of Internal Medicine, National Hospital Organization Kinki-Chuo Chest Medical Center, Japan
  • Sugimoto Chikatoshi
    Clinical Research Center, National Hospital Organization Kinki-Chuo Chest Medical Center, Japan
  • Arai Toru
    Clinical Research Center, National Hospital Organization Kinki-Chuo Chest Medical Center, Japan
  • Akira Masanori
    Clinical Research Center, National Hospital Organization Kinki-Chuo Chest Medical Center, Japan Department of Radiology, National Hospital Organization Kinki-Chuo Chest Medical Center, Japan
  • Inoue Yoshikazu
    Clinical Research Center, National Hospital Organization Kinki-Chuo Chest Medical Center, Japan

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<p>Cryptogenic organizing pneumonia (COP) generally responds well to corticosteroids with a favorable outcome. Rare cases of organizing pneumonia are rapidly progressive. Yousem et al. studied pathologic predictors of idiopathic bronchiolitis obliterans organizing pneumonia/COP with an unfavorable prognosis. Beardsley and Rassl proposed the name fibrosing organizing pneumonia (FOP). A 74-year-old female non-smoker presented with a 2-week history of dry cough followed by dyspnea and a fever. The clinical course was fulminant, but we successfully performed bronchoscopy. After the diagnosis of FOP, we treated the patient with mechanical ventilation and high-doses of steroids/immunosuppressants, which improved the disease. </p>

収録刊行物

  • Internal Medicine

    Internal Medicine 56 (10), 1185-1191, 2017

    一般社団法人 日本内科学会

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