先天性無トランスフェリン血症の治療  主にアポトランスフェリンの効果

書誌事項

タイトル別名
  • Replacement Therapy for a Patient with Congenital Atransferrinemia
  • センテンセイ ム トランスフェリン ケッショウ ノ チリョウ オモニ アポトラ
  • —主にアポトランスフェリンの効果—

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抄録

Congenital atransferrinemia is a rare disease which exhibits an extreme hypochromic anemia due to transferrin deficiency. We have been following this case for about 17 years but we have experienced considerable difficulties with the side effects of repeated blood and plasma preparations transfusion. However, in October of 1977 we obtained continuous use of this drug, we have achieved a remarkable improvement of anemia. At first, we administered a dosage of 300mg/day. Then we decreased the dosage and we now are administering 1,500mg/week. Although the level of serum transferrin was low despite this therapy, it produced a sufficient effect on anemia. No side effects due to this therapy have been observed. Although Apotransferrin therapy is not yet established, we thought it useful to report on our clinical experinece with this agent in regard to the dosage and its effectiveness in treating congenital atransferrinemia.

収録刊行物

  • 臨床血液

    臨床血液 22 (11), 1708-1713, 1981

    一般社団法人 日本血液学会

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