髄外造血所見を伴う皮膚浸潤を認めた骨髄異形成/骨髄増殖性腫瘍 分類不能型

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書誌事項

タイトル別名
  • Cutaneous extramedullary hematopoiesis associated with myelodysplastic/myeloproliferative neoplasm, unclassifiable
  • ズイガイ ゾウケツ ショケン オ トモナウ ヒフ シンジュン オ ミトメタ コツズイイケイセイ/コツズイ ゾウショクセイ シュヨウ ブンルイ フノウガタ

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Cutaneous extramedullary hematopoiesis has been reported in a small number of patients with myelofibrosis. A 79-year-old male with JAK2V617F-positive myelodysplastic/myeloproliferative neoplasm, unclassifiable (MDS-MPN-U), presented with multiple skin lesions. The skin lesions were papulonodular, reddish brown, and elastic hard on palpation. Based on a lesion biopsy, cutaneous extramedullary hematopoiesis associated with MDS/MPN-U was diagnosed. He died four months later due to exacerbation of MDS/MPN-U. Cutaneous invasion might be associated with progressive disease and a poor prognosis for MDS/MPN-U, as it is for myelofibrosis.

収録刊行物

  • 臨床血液

    臨床血液 56 (7), 911-914, 2015

    一般社団法人 日本血液学会

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