頚部リンパ節腫脹を来した血球どん食症候群例

• 神前 英明

  滋賀医科大学耳鼻咽喉科学教室

• 田中 寛

  市立長浜病院耳鼻咽喉科

• 谷口 一浩

  市立長浜病院耳鼻咽喉科

• 奥田 哲也

  市立長浜病院内科

• 北嶋 和智

  滋賀医科大学耳鼻咽喉科学教室

書誌事項

タイトル別名

• A Case of Hemophagocytic Syndrome with Cervical Lymphadenopathy.

抄録

A 16-year-old male was admitted to our hospital in July 23, 1999, because of high fever and cervical lymphadenopathy. Although he was treated with antibiotics, his fever persisted and his laboratory data revealed leukopenia and thrombocytopenia. Bone marrow puncture was perfomed and showed increased numbers of mature histiocytosis with hemophagocytosis and diagnosis of hemophagocytic syndrome was made. He was given pulse therapy with methylprednisolone and completely recovered after the treatment and was discharged 34 days after admission.<br>Hemophagocytic syndrome presents with symptoms of fever, cytopenia, liver dysfunction and coagulopathy and it is characterized by systemic proliferation of benign hemophagocytic histiocytosis in the bone marrow, lymph nodes, liver and spleen.<br>Hemophagocytosis is induced by cytokines due to activated T-lymphocytes and macrophages. The prognosis in hemophagocytic syndrome varies from good to poor; thus, early diagnosis and early treatment are important.

収録刊行物

• 耳鼻咽喉科臨床

  耳鼻咽喉科臨床 94 (5), 469-474, 2001

  耳鼻咽喉科臨床学会

キーワード

• hemophagocytic syndrome
• lymphadenopathy
• cytopenia

詳細情報

• CRID: 1390001204262001280
• NII論文ID: 10008096579
• NII書誌ID: AN00107089
• DOI: 10.5631/jibirin.94.469
• ISSN: 18844545
• ISSN: 00326313
• Web Site: https://search.jamas.or.jp/link/ui/2001243263
• 本文言語コード: ja
• データソース種別:
  • JaLC
  • Crossref
  • CiNii Articles
• 抄録ライセンスフラグ: 使用不可