巨大後腹膜嚢胞状リンパ管腫の1例  [in Japanese] A CASE OF GIANT RETROPERITONEAL CYSTIC LYMPHANGIOMA  [in Japanese]

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Abstract

症例は7歳女児で,腹囲の増大と腹満感が出現し来院.触診にて圧痛はなく,腹水貯留を思わせる波動を触知した.超音波, CT, MRIなどの検査にて,左上腹部を中心に骨盤腔まで達する,境界明瞭な多房性の巨大な嚢胞を認め,脾臓は左側へ,胃,小腸及び大腸は右側へ圧排されていた.以上の所見から後腹膜嚢胞と診断し,開腹術を施行した.腹腔内には,脾動脈の分枝により栄養された,巨大な軟らかい嚢胞が後腹膜,膵前面に存在し,周囲との癒着は軽度で摘出は容易であった.摘出した嚢胞は大きさ25×13×7cmで,重量は1,600gであった.病理組織学的には,嚢胞内腔は一層の扁平ないし立方状の内皮に覆われ,壁には平滑筋線維組織及び巣状のリンパ球浸潤や拡張した血管,リンパ管が認められ,嚢胞状リンパ管腫と診断した.

A 7-year-old girl was admitted to the clinic because of abdominal distension and fullness. On physical examination fluctuation was noted, but no mass was palpated in the abdomen. An echogram, CT scan and MRI revealed a giant multilocular and well-demarcated cyst extended up to the left epigastric lesion and down into the iliac fossa. Upper GI series showed the mechanical displacement and compression of the stomach and small intestine by the cyst. At laparotomy, a large soft cystic tumor was found in the retroperitoneum anterior to the pancreas without adhesion and fixation to the other organs, and it could be easily removed. The resected specimen was 25×13×7cm in size and 1600g in weight. Microscopi-cally, the tumor was consisted of multicystic spaces lined by a squamous or cuboidal epithelium, with focal lymphocytic infiltration and dilatated capillaries or lymphatics. Histopathological diagnosis was cystic lymphangioma of the retroperitoneum.

Journal

  • The journal of the Japanese Practical Surgeon Society

    The journal of the Japanese Practical Surgeon Society 56(8), 1713-1716, 1995-08-25

    Japan Surgical Association

References:  24

Cited by:  1

Codes

  • NII Article ID (NAID)
    10008515223
  • NII NACSIS-CAT ID (NCID)
    AN00198696
  • Text Lang
    JPN
  • Article Type
    Journal Article
  • ISSN
    03869776
  • Data Source
    CJP  CJPref  J-STAGE 
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