先天性多形皮膚萎縮症に合併した食道狭窄の1例 [in Japanese] A CASE OF ESOPHAGEAL STENOSIS WITH CONGENITAL POIKILODERMA [in Japanese]
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Congenital poikiloderma is an extremely rare entity which causes various dysplasiae of the skin from chidhood. Recently we experienced a case of esophageal stenosis associated with congenital poikiloderma.<br> A 39-year-old woman was seen at the hospital because of dysphagia which began in her childhood. There were previous histories of stenosis of the vaginal orifice and idiopathic portal hypertension. Upper gastrointestinal series revealed figuratus stenoses at the enterance and upper portion of the esophagus. Endoscopically the arytenoid portoin of the larynx was membranous and the entrance of the esophagus was very narrow, so esophageal bougienage was required. After twice bougienage, the stenosis was improved to permit the insertion of a gastrofiber scope. Her dysphagia disappeared. She can take foods orally and is followed on an ambulant basis.
- The journal of the Japanese Practical Surgeon Society
The journal of the Japanese Practical Surgeon Society 58(2), 369-372, 1997-02-25
Japan Surgical Association