複雑部分発作重積を示したdouble cortex syndromeの1女児例 [in Japanese] A Case of Double Cortex Syndrome Accompanied by Complex Partial Status Epilepticus [in Japanese]
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頻回の複雑部分発作を示すdouble cortex syndromeの12歳女児例を報告した。発作様式は, 眼球の共同偏視を伴う数分間の意識減損が断続的に出現するものであり, 意識減損に一致して左後頭部, 頭頂部付近もしくは左前頭部の律動波から始まる発作時脳波が記録された。意識障害は6時間持続したが, ダイアゼパムの静注にて頓挫した。double cortex syndromeでは種々の痙攣発作を認めるが, 複雑部分発作重積を伴ったものとしては本例が最初の報告と思われる。
We report a 12-year-old girl with double cortex syndrome. She was moderately retarded and had bilateral tonic seizures of upper extremities and atonic seizures of lower extremities with consciouness disturbances. An interictal EEG showed two foci of spikes, left frontpolar and left posteriortemporal.<BR>She was hospitalized due to fluctuating disturbance of consciousness from a nearly normal to an almost unresponsive state. An electro-encephalogram recorded during the unresponsive state disclosed a diffuse but posteriorly predominant 4-5 Hz hypersynchronous waves that began as a 10-11 Hz focal rhythmic waves at left parietooccipital or frontal area. 2-3 Hz spike and wave complex, following right frontal dominant 12-13 Hz wave, sometimes accompanied this high voltage wave. This pattern continued for a few minutes and the consciousness returned to a nearly normal state as these waves disappeared. This complex partial status was composed of complex partial seisure for some minutes long and interictal state, in which the consciousness did not return to normal. These states were periodically repeated in a few minutes and were effectivey controlled by intravenous diazepam.<BR>Although double cortex syndrome is a rare migratory disorder, it has often been reported together with intractable epilepsy. As far as we know, this is the first case of double cortex syndrome accompanied by complex partial status epilepticus.
- Journal of the Japan Epilepsy Society
Journal of the Japan Epilepsy Society 13(3), 227-232, 1995-10-31
JAPAN EPILEPSY SOCIETY