Partial idiopathic epileptic syndrome of frontal lobe origin (Vigevano and Fusco)と思われる1例 [in Japanese] A Case of Partial Idiopathic Epileptic Syndrome of Frontal Lobe Origin (Vigevano and Fusco) [in Japanese]
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9歳女児の睡眠中の異常行動を脳波・ビデオで同時記録し検討した結果, 前頭葉起源の発作と考えられた. 発作は就寝1時間後より頻発し, 両眼を強く閉じ, 両上肢を挙上し, 全身を律動的に揺するようだった. 知能は正常で, 神経学的な異状はなく, 頭部CT, MRI, SPECTは全て正常だった. 発作間欠期睡眠脳波で中心部右側家優位に低振幅鋭波が見られた. 終夜脳波で17回の完全な発作が記録され, 一部の発作で右前頭部起始と思われた. 抗てんかん薬投与による発作抑制は極めて容易だった. 本例はてんかんの家族歴はないが, 1993年にVigevano and Fuscoが提唱した前頭葉起源の小児良性部分てんかんと思われた. 本例は本邦最初の上記疾患例報告と思われるが, 非てんかん性発作として見逃されている例が多いかも知れない.
A peculiar behavior of a nine-year-old girl during sleep was captured by video EEG simultaneous recording system and investigated. It was proved that she was having epileptic seizures with frontal lobe origin. Her seizures began about one hour after falling asleep and occurred frequently during all night sleep. The seizure manifestations seemed to be tight eye closure, elevation of bilateral arms and rhythmi cal whole body shaking. She had no mental deficiency nor other neurological problems. Her brain CT, MRI and SPECT scans were entirely normal. Interictal EEG showed several low amplitude sharp activities predominating on the right frontal central area. Seventeen complete epileptic seizures were captured in a full-night EEG recording. And a part of ictal records revealed right frontal origin. Seizure control by antiepile ptic drugs was quite ideal. Although there is no other epileptic relatives, this condition was regarded to be the partial idiopathic epileptic syndrome of frontal lobe origin proposed by Vigevano and Fusco in 1993. This must be the first report of the syndrome in Japan. There may be not a few patients looked over as having nonepileptic seizures.
- Journal of the Japan Epilepsy Society
Journal of the Japan Epilepsy Society 14(1), 19-24, 1996-02-29
JAPAN EPILEPSY SOCIETY