自己誘発図形過敏てんかんの1例  [in Japanese] Self-Inducfed Pattern-Sensitive Epilepsy  [in Japanese]

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Abstract

まれな自己誘発図形過敏てんかんの1例を報告した。現在13歳の女児。けいれんの家族歴はない。6歳より網戸、縞模様等を見つめるとミオクロニー発作をきたすようになった。当初より発作の多くは自己誘発と思われ、10歳以降は明らかに自己誘発のみとなった。これらのミオクロニー発作と2回の全般発作以外の発作型はなく、光過敏発作もなかった。また、図形過敏以外で自然におこる発作もなかった。発作問欠時脳波では全般性棘徐波複合の群発を認めたが、光過敏は明らかではなかった。発作時脳波は全般性多棘波複合の群発であった。神経学的所見、頭部CTには異常を認めなかったが、新版K式発達検査で、認知・適応指数59、言語・社会指数80、全IQ 71と境界域精神遅滞があった。認知・適応指数の低さは、視覚的記憶の不良のためであった。また図形に対する執着的な行動が見られた。バルプロ酸投与により12歳より発作は抑制された。

A 6-year-old girl developed self-induced pattern-sensitive epilepsy. There is no family history of epilepsy. At 6 years, she developed myoclonic jerks mainly on voluntary viewing of patterns such as her mother's vertically-striped clothes and a mesh of screen windows. Neither spontaneous nor photosensitive seizures occurred. Her seizures remained myoclonic except two generalized tonic-clonic seizures at ages 7 and 11. After the age of 10, the seizures occurred exclusively by self-induction. Interictal EEGs showed generalized spike-wave complexes but no photosensitivity. Ictal EEGs showed a generalized polyspike-wave complex. Computed tomography on the head revealed no abnormalities. Her self-induced seizures were controlled with valproate by the end of her 12th year. However, she had obsessive interest in patterns until age 12. She did not have other behavioral problems, but her intelligence quotient was 71 on the Kyoto Scale of Psychological Development. Her visual memory was especially poor in the test. She is now 13 years old and still on valproate. She is seizure-free and shows no more obsessive behavior toward patterns.

Journal

  • Journal of the Japan Epilepsy Society

    Journal of the Japan Epilepsy Society 16(2), 127-131, 1998-06-30

    JAPAN EPILEPSY SOCIETY

References:  9

Codes

  • NII Article ID (NAID)
    10008556009
  • NII NACSIS-CAT ID (NCID)
    AN10043823
  • Text Lang
    JPN
  • Article Type
    NOT
  • ISSN
    09120890
  • Data Source
    CJP  J-STAGE 
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