Unique Electroencephalographic Change of Acute Encephalopathy in Glutaric Aciduria Type 1
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- Fujimoto Shinji
- Department of Laboratory Medicine, Nagoya City University Medical School Department of Pediatrics, Nagoya City University Medical School
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- Shibata Hideo
- Department of Laboratory Medicine, Nagoya City University Medical School
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- Sugiyama Naruji
- Department of Pediatrics, Nagoya City University Medical School
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- Ohba Satoru
- Department of Pediatrics, Nagoya City University Medical School
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- Togari Hajime
- Department of Pediatrics, Nagoya City University Medical School
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- Wada Yoshiro
- Department of Pediatrics, Nagoya City University Medical School
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Abstract
We report the peculiar serial electroencephalographic (EEG) findings in a 7-year-old boy with glutaric aciduria type 1 during an episode of acute encephalopathy. The patient developed Reye-like syndrome triggered by cellulitis. Cranial magnetic resonance imaging demonstrated diffuse softening of cerebral hemisphere. The EEG on the day following onset of acute encephalopathy showed suppression burst pattern including continuous 14-15 Hz rhythmic waves at first. Then, periodic synchronous discharge appeared and lasted for about 40 minutes. Periodic synchronous discharge finally disappeared and nearly total electrocerebral silence continued. There have been no reports indicating such a change of EEG in a short period. The serial EEG changes probably reflect the process of electrical death of neurons in cerebral hemispheres.
Journal
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- The Tohoku Journal of Experimental Medicine
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The Tohoku Journal of Experimental Medicine 191 (1), 31-38, 2000
Tohoku University Medical Press
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Details 詳細情報について
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- CRID
- 1390282679218111360
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- NII Article ID
- 10013014980
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- NII Book ID
- AA00863920
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- COI
- 1:STN:280:DC%2BD3M%2FitlSlsA%3D%3D
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- ISSN
- 13493329
- 00408727
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- PubMed
- 10896037
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- Text Lang
- en
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- Data Source
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- JaLC
- Crossref
- PubMed
- CiNii Articles
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- Abstract License Flag
- Disallowed