Oro-Facial Findings of a Patient Affected with the Bloch-Sulzberger Syndrome Based on Longitudinal Observation

DOI 4 Citations 30 References
  • Nonaka Kazuaki
    Department of Pediatric Dentistry, Kyushu University Faculty of Dentistry
  • Sasaki Yasunori
    Department of Pediatric Dentistry, Kyushu University Faculty of Dentistry
  • Yanagita Ken-ichi
    Department of Pediatric Dentistry, Kyushu University Faculty of Dentistry
  • Yatsuda Naomi
    Department of Pediatric Dentistry, Kyushu University Faculty of Dentistry
  • Nakata Minoru
    Department of Pediatric Dentistry, Kyushu University Faculty of Dentistry

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  • Bloch-Sulzberger Syndromeの患児の経年的観察による歯科的所見

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Abstract

Bloch-Sulzberger syndrome is an X-linked dominant heritable disorder with various systemic and oral problems. It is also called incontinentia pigmenti because it is easily characterized by peculiar pigmentation of the skin of infants. Intra-oral clinical findings were mainly manifested due to delay of tooth eruption, microdontia and anodontia. A three-year-old girl affected with the Bloch-Sulzberger syndrome was observed for nine years and showed the following findings.<BR>1) Brown hyperpigmentation in the skin of the face, the upper arm and the tongue tip.<BR>2) Alopecia with scarring on the crown of the head.<BR>3) Weak eyesight.

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