A CASE OF VON RECKLINGHAUSEN'S DISEASE ASSOCIATED WITH HEMOTHORAX

• DOMEN Hiromitsu

  Department of Surgery, Obihiro Kosei Hospital

• ONO Koichi

  Department of Surgery, Obihiro Kosei Hospital

• SHIONO Tsuneo

  Department of Surgery, Obihiro Kosei Hospital

• FUJIMORI Masaru

  Department of Surgery, Obihiro Kosei Hospital

• SEKISHITA Yoshiaki

  Department of Surgery, Obihiro Kosei Hospital

• KONDO Satoshi

  Department of Surgical Oncology, Hokkaido University

Bibliographic Information

Other Title

• 血胸を合併したｖｏｎ　Ｒｅｃｋｌｉｎｇｈａｕｓｅｎ病の１例

Abstract

A 64-year-old man, diagnosed as having von Recklinghausen's disease about 30 years earlier, was brought into the hospital because of severe pain from the left lateral thoracic region to the back on June 16, 2002. Chest x-ray showed pleural effusion in the left lung and abnormal bone deformity in the left 6^th to 8^th intercostal space. Chest CT scan revealed bleeding from the posterior intercostl artery. Accordingly an emergency operation was performed. Thoracotomy at the 7^th costal bed disclosed about 3200ml of bleeding in the thoracic cavity. The cause was arterial bleeding from a schwannoma of the 6^th intercostal nerve. Besides, multiple schwannomas were seen in the 7^th intercostal nerve, but entire tumors were difficult to be removed so that the tumor of the 6^th intercostal nerve was removed as complete as possible. Then the intercostal artery and veins and intercostal nerves were ligated.<br> Von Recklinghausen's disease is the most common autosomal dominant hereditary disease and affects one out of 3000 persons. However, the disease associated with hemothorax in so rare that only 10 cases have been reported in Japan. Five patients of them died and hence prompt diagnosis and surgery would be mandatory.

Journal

• Nihon Rinsho Geka Gakkai Zasshi (Journal of Japan Surgical Association)

  Nihon Rinsho Geka Gakkai Zasshi (Journal of Japan Surgical Association) 66 (6), 1295-1298, 2005

  Japan Surgical Association

Keywords

• von Recklinghausen病
• 血胸
• 神経線維腫

Details

• CRID: 1390001204848653568
• NII Article ID: 130003604502
• NII Article ID: 10016461003
• NII Book ID: AA11189709
• DOI: 10.3919/jjsa.66.1295
• ISSN: 18825133
• ISSN: 13452843
• ISSN: http://id.crossref.org/issn/13452843
• Web Site: http://www.jstage.jst.go.jp/article/ringe1998/66/6/66_6_1295/_pdf
• Web Site: https://search.jamas.or.jp/link/ui/2005214135
• Text Lang: ja
• Data Source:
  • JaLC
  • Crossref
  • CiNii Articles
• Abstract License Flag: Disallowed