Ciliated hepatic foregut cyst:report of a case and a summary of the 24 cases reported in Japan

• MANNAMI Tomohiko

  Department of Gastroenterology, National Hospital Organization Okayama Medical Center

• OHFUJI Yoshihiro

  Department of Gastroenterology, National Hospital Organization Okayama Medical Center

• FUJIWARA Keiko

  Department of Gastroenterology, National Hospital Organization Okayama Medical Center

• ENOMURA Katsuhiro

  Department of Gastroenterology, National Hospital Organization Okayama Medical Center

• OHTA Tetsuya

  Department of Surgery, National Hospital Organization Okayama Medical Center

• KUNISUE Hironori

  Department of Surgery, National Hospital Organization Okayama Medical Center

• NOMURA Shuichi

  Department of Surgery, National Hospital Organization Okayama Medical Center

• EGUCHI Kaori

  Department of Pathology, National Hospital Organization Okayama Medical Center

• ODA Wakako

  Department of Pathology, National Hospital Organization Okayama Medical Center

• YAMADORI Ichiro

  Department of Pathology, National Hospital Organization Okayama Medical Center

• YAMASHITA Haruhiro

  Department of Gastroenterology, National Hospital Organization Okayama Medical Center

Bibliographic Information

Other Title

• 線毛性前腸性肝嚢胞(ciliated hepatic foregut cyst）の1例-本邦報告例24例の検討-

Abstract

We report a 52-year-old patient with a small hepatic mass which was ultrasonographically anechoic with scattered high echoic spots, and appearing slightly hyperattenuating relative to the surrounding parenchyma on unenhanced CT scans. Laparotomy revealed that the lesion was a unilocular cyst containing a mucinous fluid. The histologic diagnosis was ciliated hepatic foregut cyst (CHFC). The CHFC is a rare congenital cystic tumor which derives from the embryologic foregut. Up to 2006, only 24 cases, including our case, had been reported in Japan. The patients were 13 men and 11 women, aged between 41 years and 79 years. All of the lesions were solitary and unilocular. In 22 cases, the CHFC was located in the medial segment of the left lobe, mostly just beneath the hepatic surface. In all 24 Japanese cases, the cystic wall was benign histologically. However, reports of 3 malignant cases overseas indicates we should treat this disease cautiously.<br>

Journal

• Nippon Shokakibyo Gakkai Zasshi

  Nippon Shokakibyo Gakkai Zasshi 105 (2), 235-243, 2008

  The Japanese Society of Gastroenterology

Keywords

• 線毛性前腸性肝嚢胞
• 肝嚢胞性疾患
• ciliated hepatic foregut cyst

Details

• CRID: 1390001206399343616
• NII Article ID: 10021270501
• NII Book ID: AN00192124
• DOI: 10.11405/nisshoshi.105.235
• ISSN: 13497693
• ISSN: 04466586
• Web Site: https://search.jamas.or.jp/link/ui/2008136698
• Text Lang: ja
• Data Source:
  • JaLC
  • CiNii Articles
• Abstract License Flag: Disallowed