IgG4-Related Sclerosing Disease

• Kurakami Kazuya

  Yamagata University

• Ohta Nobuo

  Yamagata University

• Abe Yasuhiro

  Yamagata Prefectural Central Hospital

• Watanabe Tomoo

  Yamagata University

• Ito Tsukasa

  Yamagata University

• Onoe Yoshihiro

  Onoe Clinic

• Ishida Akihiro

  Yamagata University

• Inamura Kazutoshi

  Yamagata Prefectural Kahoku Hospital

• Waki Takayoshi

  Yamagata Prefectural Shinjo Hospital

• Suzuki Yusuke

  Yamagata University

• Aoyagi Masaru

  Yamagata University

Bibliographic Information

Other Title

• ＩｇＧ４関連硬化性疾患の検討
• 臨床 IgG4関連硬化性疾患の検討
• リンショウ IgG4 カンレン コウカセイ シッカン ノ ケントウ

Abstract

We report to cases of systemic IgG4-related sclerosing disease involving the dissemination of CD4- or CD8-positive T lymphocytes and IgG4-positive plasma cells in numerous internal organs. The pancreas, bile duct, salivary glands, thyroid gland, and retroperitoneum are often permeated by IgG4-positive plasma cells, suggesting that sclerosing salivary glanditis as Mikulicz’s disease and Küttner’s tumor, autoimmune pancreatitis, sclerosing cholangitis, and retroperitoneal fibrosis are IgG4-related sclerosing phenotypes. The paucity of cases has prevented development of a conclusive treatment regimen, although oral steroid is have proven effective.<br>

Journal

• Practica Oto-Rhino-Laryngologica

  Practica Oto-Rhino-Laryngologica 103 (8), 747-754, 2010

  The Society of Practical Otolaryngology

Keywords

• IgG4-related sclerosing disease
• Mikulicz’s disease
• autoimmune pancreatitis
• steroid

Details

• CRID: 1390282679240320640
• NII Article ID: 10026493037
• NII Book ID: AN00107089
• DOI: 10.5631/jibirin.103.747
• ISSN: 18844545
• ISSN: 00326313
• NDL BIB ID: 10791381
• Web Site: https://ndlsearch.ndl.go.jp/books/R000000004-I10791381
• Web Site: https://search.jamas.or.jp/link/ui/2010317654
• Text Lang: ja
• Data Source:
  • JaLC
  • NDL
  • Crossref
  • CiNii Articles
• Abstract License Flag: Disallowed