A Case of Congenital Piriform Sinus Fistula Causing Respiratory Distress in a Newborn Infant

  • Shinnabe Akihiro
    Division of Otorhinolaryngology, National Hospital Organization Tochigi Hospital
  • Tashiro Masatsugu
    Division of Otorhinolaryngology, National Hospital Organization Tochigi Hospital
  • Habuo Noboru
    Division of Otorhinolaryngology, National Hospital Organization Tochigi Hospital
  • Sugimori Mitsuko
    Division of Pediatrics, National Hospital Organization Tochigi Hospital
  • Hagane Kazuhiko
    Division of Pediatric Surgery, National Hospital Organization Tochigi Hospital
  • Hirabayashi Ken
    Division of Pediatric Surgery, National Hospital Organization Tochigi Hospital
  • Fujino Akihiro
    Division of Pediatric Surgery, National Hospital Organization Tochigi Hospital
  • Mizutari Kunio
    Divison of Otorhinolaryngology National Hospital Organization Tokyo Medical Center

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Other Title
  • 新生児期に呼吸障害を呈した下咽頭梨状窩瘻の一例

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Abstract

A piriform sinus fistula is not usually present during the newborn period. We report a case of piriform sinus fistula causing a life-threatening respiratory obstruction in the period immediately after birth. Radiographs and computed tomography (CT) showed an air-containing retropharyngeal cyst. Cystostomy was carried out because the upper respiratory obstruction had worsened. We diagnosed a piriform sinus fistula using a laryngeal fiberscope and coloring matter. Moreover, threedimensional CT was contributory to the diagnosis. Finally, total resection of the cyst was conducted and the patient left our hospital without any obvious complications.

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