"Hydrocephalus Due to Diffuse Villous Hyperplasia of the Choroid Plexus: Case Report　（脈絡叢のび漫性絨毛過形成による水頭症　1症例報告） " Hydrocephalus Due to Diffuse Villous Hyperplasia of the Choroid Plexus : Case Report

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Abstract

雑誌掲載版症例は8ヵ月齢女児で、両側脈絡叢拡大による脳脊髄液過剰産生を原因とする水頭症を呈した。これは臨床的にび漫性絨毛過形成と診断されたが、脈絡叢乳頭腫との鑑別は困難であった。脳室腹腔短絡術を施行したが、腹水が著明に滞留した。体外ドレナージのためシャントの腹膜端を除去したところ、過剰の脳脊髄液(CSF)が採取された。CTおよびMRIでは両側側脳室における脈絡叢の著しい対称性増強を認めた。201TlCl SPECTでは早期画像と後期画像の両方で著しい取り込みがみられ、洗い出しは良好であった。CSFの検索では異型細胞等の異常は認められず、脳室心房シャントを挿入した。その結果、水頭症を良好に管理できた。

An 8-month-old female presented with hydrocephalus caused by cerebrospinal fluid (CSF) overproduction due to bilateral choroid plexus enlargement, which was clinically diagnosed as diffuse villous hyperplasia of the choroid plexus, but differentiation from bilateral choroid plexus papilloma was difficult. She initially underwent ventriculoperitoneal shunt surgery, but developed marked retention of ascites. Therefore, the peritoneal end of the shunt was removed for external drainage, but excessive CSF (1,500 ml/day) was collected. Computed tomography and magnetic resonance imaging revealed marked symmetric enhancement of the choroid plexuses in the bilateral lateral ventricles. Thallium-201 chloride single-photon emission computed tomography showed pronounced uptake on both early and delayed images, and good washout. CSF examination revealed no abnormalities such as atypical cells, and a ventriculoatrial shunt was inserted, achieving good control of the hydrocephalus.<br>

Journal

  • Neurologia medico-chirurgica

    Neurologia medico-chirurgica 51(6), 437-441, 2011-06-15

    The Japan Neurosurgical Society

References:  22

Codes

  • NII Article ID (NAID)
    10029138205
  • NII NACSIS-CAT ID (NCID)
    AN00358613
  • Text Lang
    ENG
  • Article Type
    NOT
  • ISSN
    04708105
  • DOI
    10.2176/nmc.51.437
  • Data Source
    CJP  IR  J-STAGE 
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