両側水腎症による急性腎不全をきたし,ステロイド療法が有効であった特発性後腹膜線維症の1例  [in Japanese] A Case of Idiopathic Retroperitoneal Fibrosis Presenting as Acute Renal Failure Due to Bilateral Hydronephrosis, which Responded to Steroid Therapy  [in Japanese]

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Author(s)

Abstract

両側水腎症による急性腎不全をきたしたが,ステロイド療法が奏効した特発性後腹膜線維症の1例を報告する.症例は76歳男性で主訴は曖気,食思不振である.血液検査では炎症と腎不全の所見を認め,また腹部超音波検査では両側水腎症がみられたー逆行性腎盂尿管造影では両側尿管の偏位と狭窄を,さらに腹部CT検査では大動脈および総腸骨動脈周囲の軟部組織影を認めた.以上の検査結果から特発性後腹膜線維症と診断し,ステロイド療法を開始したところ,3ヶ月後には全身症状および画像所見の改善がみられた.本例には大動脈壁の著明な石灰化がみられ,本症との関連が示唆された.

We report a case of idiopathic retroperitoneal fibrosis(IRF) with acute renal failure due to bilateral hydronephrosis effectively treated with steroid therapy. The patient was a 76-year-old male who came to us complaining of excessive belching and anorexia. Laboratory data showed signs of inflammation and renal failure. Abdominal ultrasonography demonstrated bilateral hydronephrosis, and retrograde urography revealed stenosis and medial deviation of the bilateral ureters. Computed tomographic(CT) imaging showed a dense soft tissue mass located around the abdominal aorta and iliac arteries, with calcification in the wall of the abdominal aorta. Following the radiographic findings, a diagnosis of IRF was made. Management with steroid therapy improved general symptoms and radiographic findings together with laboratory findings. Prominent calcification in the wall of the abdominal aorta suggested that the atherosclerosis was related to IRF.

Journal

  • Acta medica Hyogoensia

    Acta medica Hyogoensia 32(1), 105-109, 2007-12

    Hyogo College of Medicine

Codes

  • NII Article ID (NAID)
    110006992576
  • NII NACSIS-CAT ID (NCID)
    AN00209420
  • Text Lang
    JPN
  • ISSN
    03857638
  • Data Source
    NII-ELS 
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