赤血球表面膜免疫グロブリン定量により診断し得たＥｖａｎｓ症候群の１乳児例

• 成田 努

  滋賀医科大学小児科 近江八幡市民病院小児科

• 東野 克巳

  滋賀医科大学小児科

• 多賀 崇

  滋賀医科大学小児科

• 太田 茂

  滋賀医科大学小児科

• 島田 司巳

  滋賀医科大学小児科

• 島田 佐和子

  済生会滋賀病院小児科

• 山本 徹

  済生会滋賀病院小児科

書誌事項

タイトル別名

• An Infantile Case of Evans Syndrome Confirmed by Quantitative Analysis of Surface Immune Globulin on Red Blood Cells.

抄録

We report the case of an infant with Evans syndrome. She was admitted to our hospital with complaints of pyrexia, anemia and thrombocytopenia at 6 months of age. She developed hemolytic anemia, however she was negative for both direct antiglobulin and cold-reactive antibodies. We subsequently confirmed the diagnosis of Evans syndrome by measuring the amount of surface immune globulins on red blood cells (RBC-associated IgG) and the bone marrow findings, i.e. increase of megakaryocytes (816/μl) and absence of platelet production. PAIgG remained normal and anti-platelet antibody was negative. It is important to measure the surface immunoglobulins on RBC surface in patients with hemolytic anemia who show a negative Coombs test.

収録刊行物

• 日本小児血液学会雑誌

  日本小児血液学会雑誌 10 (5), 367-370, 1996

  特定非営利活動法人　日本小児血液・がん学会

キーワード

• autoimmune hemolytic anemia
• idiopathic thrombocytopenic purpura
• Evans syndrome
• negative Coombs test
• RBC-associated IgG

詳細情報

• CRID: 1390282679319917568
• NII論文ID: 130004345466
• NII論文ID: 10012260582
• NII書誌ID: AN10080852
• DOI: 10.11412/jjph1987.10.367
• ISSN: 18844723
• ISSN: 09138706
• Web Site: https://search.jamas.or.jp/link/ui/1997084037
• 本文言語コード: ja
• データソース種別:
  • JaLC
  • CiNii Articles
• 抄録ライセンスフラグ: 使用不可