A Case of Marfan Syndrome with Facial Asymmetry Treated by Simultaneous Bimaxillary Distraction Osteogenesis

• KIMIZUKA SACHIKO

  Department of Oral & Maxillofacial Surgery, School of Dental Medicine, Tsurumi University Department of Oral and Maxillofacial Surgery, Yokohama City University Medical Center

• FUKUYAMA EIJI

  JOY Orthodontic Clinic Orthodontic Science, Division of Oral Health Sciences, Graduate School, Tokyo Medical and Dental University

• YONEMITSU IKUO

  Orthodontic Science, Division of Oral Health Sciences, Graduate School, Tokyo Medical and Dental University

• SHIMAZAKI KAZUO

  Orthodontic Science, Division of Oral Health Sciences, Graduate School, Tokyo Medical and Dental University

• OMURA SUSUMU

  Department of Oral and Maxillofacial Surgery, Yokohama City University Medical Center

• HAMADA YOSHIKI

  Department of Oral & Maxillofacial Surgery, School of Dental Medicine, Tsurumi University

• TOHNAI IWAI

  Department of Oral and Maxillofacial Surgery, Yokohama City University Graduate School of Medicine

Bibliographic Information

Other Title

• 顔面非対称に対して上下顎同時骨延長術を適用したMarfan症候群の1例

Abstract

A 19-year-old male with Marfan syndrome (MFS) was referred to our hospital for improvement of his facial asymmetry. Orthognathic surgery was planned because the cardiovascular and thoracic abnormalities were relatively mild. The patient initially underwent pre-operative orthodontic treatment, and then the surgery was performed under careful control of the cardiovascular and pulmonary function. After a combination of Le Fort I osteotomy and bilateral sagittal splitting ramus osteotomy, a distractor was placed on the hypoplastic side of the maxilla. The activation of the distractor resulted in gradual rotation of the maxillomandibular complex using intermaxillary fixation. This allowed decanting of the occlusal plane with displacement of the chin position to the opposite side, leading to an improvement in the facial asymmetry. The postoperative course was uneventful. Over a follow-up period of 11 years, the facial symmetry and the occlusion have been stable.

Journal

• The Japanese Journal of Jaw Deformities

  The Japanese Journal of Jaw Deformities 25 (1), 49-55, 2015

  THE JAPANESE SOCIETY FOR JAW DEFORMITIES

Keywords

• simultaneous bimaxillary distraction osteogenesis
• facial asymmetry
• Marfan syndrome

Details

• CRID: 1390282679429122432
• NII Article ID: 130005066068
• DOI: 10.5927/jjjd.25.49
• ISSN: 18845045
• ISSN: 09167048
• Web Site: https://search.jamas.or.jp/link/ui/2015237064
• Text Lang: ja
• Data Source:
  • JaLC
  • Crossref
  • CiNii Articles
  • KAKEN
• Abstract License Flag: Disallowed