Werner Syndrome and Diabetes Mellitus Accompanied by Adrenal Cortex Cancer

  • Nishioka Momoyo
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Kamei Shinji
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Kinoshita Tomoe
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Sanada Junpei
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Fushimi Yoshiro
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Irie Shintaro
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Hirata Yurie
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Tanabe Akihito
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Hirukawa Hidenori
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Kimura Tomohiko
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Obata Atsushi
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Tatsumi Fuminori
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Kohara Kenji
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Shimoda Masashi
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Nakanishi Shuhei
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Mune Tomoatsu
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Kaku Kohei
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan
  • Kaneto Hideaki
    Department of Diabetes, Endocrinology and Metabolism, Kawasaki Medical School, Japan

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抄録

<p>Werner syndrome is a rare genetic disease characterized by progeria, diabetes mellitus, cataracts and various types of malignancy. However, there are few reports showing adrenal cortex cancer in subjects with Werner syndrome. We herein report an extremely rare case of Werner syndrome accompanied by adrenal cortex cancer. Based on the data obtained from blood samples, computed tomography, magnetic resonance imaging and 131I adosterol scintigraphy, we diagnosed this subject with adrenal cortex cancer and Cushing's syndrome. Since the prognosis of adrenal cancer is very poor, we should be aware of the possibility of adrenal cancer occurring in subjects with Werner syndrome. </p>

収録刊行物

  • Internal Medicine

    Internal Medicine 56 (15), 1987-1992, 2017

    一般社団法人 日本内科学会

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